Fasting reveals largely intact systemic lipid mobilization mechanisms in respiratory chain complex III deficient mice
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چکیده
منابع مشابه
Fasting induces prominent proteomic changes in liver in very long chain Acyl-CoA dehydrogenase deficient mice
Very long chain acyl-CoA dehydrogenase (VLCAD) deficiency (VLCADD) is a clinically heterogeneous disorder of mitochondrial fatty acid β-oxidation usually identified through newborn screening. Genotype-phenotype correlations have been defined, but considerable clinical heterogeneity still exists. Symptoms are often induced by physiological stress such as fasting or intercurrent illness, setting ...
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ژورنال
عنوان ژورنال: Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease
سال: 2020
ISSN: 0925-4439
DOI: 10.1016/j.bbadis.2019.165573